Blood and Urine Screening for Metabolic Abnormalities in Patients With Donnai-Barrow Syndrome (DBS) Who Have Mutations in the Gene LRP2

This study is currently recruiting participants.
Verified January 2012 by Massachusetts General Hospital
Sponsor:
Collaborator:
Information provided by (Responsible Party):
Barbara R. Pober, Massachusetts General Hospital
ClinicalTrials.gov Identifier:
NCT01509287
First received: January 10, 2012
Last updated: August 21, 2012
Last verified: January 2012

January 10, 2012
August 21, 2012
March 2010
January 2015   (final data collection date for primary outcome measure)
Measuring blood and urine compounds, such as vitamin A [ Time Frame: 5 years ] [ Designated as safety issue: No ]
Measuring vitamin A, Retinol Binding Protein, and other compounds taken up by LRP2.
Vitamin A level [ Designated as safety issue: No ]
Measuring vitamin A and Retinol Binding Protein levels. Measuring other compounds taken up by LRP2.
Complete list of historical versions of study NCT01509287 on ClinicalTrials.gov Archive Site
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Blood and Urine Screening for Metabolic Abnormalities in Patients With Donnai-Barrow Syndrome (DBS) Who Have Mutations in the Gene LRP2
Not Provided

The project focuses on the genetics and metabolism of Donnai Barrow Syndrome (DBS).

The purpose of this research study is to learn more about the absorption of certain nutrients and compounds in persons with DBS, as well as their family members. This knowledge may provide a better understanding of normal and abnormal metabolism in DBS. We anticipate this may lead to improved outcomes, and possibly even new treatments, for individuals with DBS in the future.

Participation involves collecting information about the medical problems in your family member with DBS as well as collecting blood, urine and possibly saliva samples. In order to participate in this study, we will work closely with your local doctor or doctors. Mutation testing for the gene known to cause DBS (LRP2) is conducted on patients that pass an initial screen.

Observational
Observational Model: Case-Only
Time Perspective: Cross-Sectional
Not Provided
Retention:   Samples With DNA
Description:

Urine, saliva and blood samples are collected.

Non-Probability Sample

Any individual that is clinically suspected to have Donnai Barrow Syndrome.

Donnai Barrow Syndrome
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Index cases are individuals with DBS.
Index cases are individuals diagnosed with DBS. We will also recruit parents and unaffected siblings of individuals with DBS, whenever possible.
Not Provided

*   Includes publications given by the data provider as well as publications identified by ClinicalTrials.gov Identifier (NCT Number) in Medline.
 
Recruiting
70
January 2016
January 2015   (final data collection date for primary outcome measure)

Inclusion Criteria:

  • Clinically suspected Donnai Barrow Syndrome

Exclusion Criteria:

  • Donnai Barrow Syndrome patient is no longer alive, and urine or DNA sample are not available
Both
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No
Contact: Anna Frangulov, B.S. 617 355 2555 DBS.Research@tch.harvard.edu
Contact: Barbara R. Pober, M.D. 617 355 8780 barbara.pober@tch.harvard.edu
United States
 
NCT01509287
2009p001589
Yes
Barbara R. Pober, Massachusetts General Hospital
Massachusetts General Hospital
National Institutes of Health (NIH)
Not Provided
Massachusetts General Hospital
January 2012

ICMJE     Data element required by the International Committee of Medical Journal Editors and the World Health Organization ICTRP